3TV8
Pharmacological Chaperoning in Human alpha-Galactosidase
Summary for 3TV8
Entry DOI | 10.2210/pdb3tv8/pdb |
Related | 1R46 1R47 3HG2 3HG3 3S5Y 3S5Z |
Descriptor | Alpha-galactosidase A, beta-D-mannopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranose, alpha-D-mannopyranose-(1-3)-beta-D-mannopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranose, ... (8 entities in total) |
Functional Keywords | pharmacological chaperone, (beta/alpha)8 barrel, carbohydrate-binding protein, glycosidase, glycoprotein, n-linked glycosylation, lysosome, hydrolase |
Biological source | Homo sapiens (human) |
Total number of polymer chains | 2 |
Total formula weight | 96436.87 |
Authors | Rogich, J.J.,Guce, A.I.,Clark, N.E.,Garman, S.C. (deposition date: 2011-09-19, release date: 2012-01-04, Last modification date: 2023-09-13) |
Primary citation | Guce, A.I.,Clark, N.E.,Rogich, J.J.,Garman, S.C. The molecular basis of pharmacological chaperoning in human alpha-galactosidase Chem.Biol., 18:1521-1526, 2011 Cited by PubMed: 22195554DOI: 10.1016/j.chembiol.2011.10.012 PDB entries with the same primary citation |
Experimental method | X-RAY DIFFRACTION (2.639 Å) |
Structure validation
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