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6XT9

Subunits BBS 1,4,8,9,18 of the human BBSome complex

Functional Information from GO Data
ChainGOidnamespacecontents
A0001895biological_processretina homeostasis
A0005102molecular_functionsignaling receptor binding
A0005113molecular_functionpatched binding
A0005119molecular_functionsmoothened binding
A0005515molecular_functionprotein binding
A0005737cellular_componentcytoplasm
A0005813cellular_componentcentrosome
A0005829cellular_componentcytosol
A0005929cellular_componentcilium
A0005930cellular_componentaxoneme
A0007601biological_processvisual perception
A0007608biological_processsensory perception of smell
A0008104biological_processintracellular protein localization
A0015031biological_processprotein transport
A0030030biological_processcell projection organization
A0031514cellular_componentmotile cilium
A0034451cellular_componentcentriolar satellite
A0034464cellular_componentBBSome
A0043001biological_processGolgi to plasma membrane protein transport
A0045444biological_processfat cell differentiation
A0045494biological_processphotoreceptor cell maintenance
A0051219molecular_functionphosphoprotein binding
A0060170cellular_componentciliary membrane
A0060271biological_processcilium assembly
A0060296biological_processregulation of cilium beat frequency involved in ciliary motility
A0061512biological_processprotein localization to cilium
A0061629molecular_functionRNA polymerase II-specific DNA-binding transcription factor binding
A1905515biological_processnon-motile cilium assembly
D0000226biological_processmicrotubule cytoskeleton organization
D0000242cellular_componentpericentriolar material
D0000281biological_processmitotic cytokinesis
D0001750cellular_componentphotoreceptor outer segment
D0001843biological_processneural tube closure
D0001895biological_processretina homeostasis
D0001917cellular_componentphotoreceptor inner segment
D0001947biological_processheart looping
D0005515molecular_functionprotein binding
D0005634cellular_componentnucleus
D0005737cellular_componentcytoplasm
D0005813cellular_componentcentrosome
D0005814cellular_componentcentriole
D0005829cellular_componentcytosol
D0005929cellular_componentcilium
D0007098biological_processcentrosome cycle
D0007286biological_processspermatid development
D0007600biological_processsensory perception
D0007601biological_processvisual perception
D0007608biological_processsensory perception of smell
D0015031biological_processprotein transport
D0016020cellular_componentmembrane
D0016358biological_processdendrite development
D0019216biological_processregulation of lipid metabolic process
D0021756biological_processstriatum development
D0021766biological_processhippocampus development
D0021987biological_processcerebral cortex development
D0030030biological_processcell projection organization
D0030534biological_processadult behavior
D0030674molecular_functionprotein-macromolecule adaptor activity
D0031514cellular_componentmotile cilium
D0032391cellular_componentphotoreceptor connecting cilium
D0032402biological_processmelanosome transport
D0032465biological_processregulation of cytokinesis
D0034451cellular_componentcentriolar satellite
D0034452molecular_functiondynactin binding
D0034454biological_processmicrotubule anchoring at centrosome
D0034464cellular_componentBBSome
D0035869cellular_componentciliary transition zone
D0036064cellular_componentciliary basal body
D0038108biological_processnegative regulation of appetite by leptin-mediated signaling pathway
D0043014molecular_functionalpha-tubulin binding
D0045444biological_processfat cell differentiation
D0045494biological_processphotoreceptor cell maintenance
D0045724biological_processpositive regulation of cilium assembly
D0046548biological_processretinal rod cell development
D0048487molecular_functionbeta-tubulin binding
D0048854biological_processbrain morphogenesis
D0050893biological_processsensory processing
D0051457biological_processmaintenance of protein location in nucleus
D0060170cellular_componentciliary membrane
D0060271biological_processcilium assembly
D0060296biological_processregulation of cilium beat frequency involved in ciliary motility
D0061512biological_processprotein localization to cilium
D0061629molecular_functionRNA polymerase II-specific DNA-binding transcription factor binding
D0071539biological_processprotein localization to centrosome
D0097730cellular_componentnon-motile cilium
D1905515biological_processnon-motile cilium assembly
H0007600biological_processsensory perception
H0009653biological_processanatomical structure morphogenesis
H0015031biological_processprotein transport
H0016020cellular_componentmembrane
H0030030biological_processcell projection organization
H0034451cellular_componentcentriolar satellite
H0034464cellular_componentBBSome
H0036064cellular_componentciliary basal body
H0060170cellular_componentciliary membrane
H0060271biological_processcilium assembly
H1905515biological_processnon-motile cilium assembly
I0000242cellular_componentpericentriolar material
I0003674molecular_functionmolecular_function
I0005515molecular_functionprotein binding
I0005737cellular_componentcytoplasm
I0005813cellular_componentcentrosome
I0005829cellular_componentcytosol
I0005929cellular_componentcilium
I0007601biological_processvisual perception
I0015031biological_processprotein transport
I0016020cellular_componentmembrane
I0030030biological_processcell projection organization
I0034451cellular_componentcentriolar satellite
I0034464cellular_componentBBSome
I0035869cellular_componentciliary transition zone
I0045444biological_processfat cell differentiation
I0060170cellular_componentciliary membrane
I0060271biological_processcilium assembly
I0061512biological_processprotein localization to cilium
I0097542cellular_componentciliary tip
J0005515molecular_functionprotein binding
J0005737cellular_componentcytoplasm
J0005829cellular_componentcytosol
J0005929cellular_componentcilium
J0015031biological_processprotein transport
J0030030biological_processcell projection organization
J0034464cellular_componentBBSome
J0036064cellular_componentciliary basal body
J0060170cellular_componentciliary membrane
J0060271biological_processcilium assembly
J0097500biological_processreceptor localization to non-motile cilium
Functional Information from SwissProt/UniProt
site_idSWS_FT_FI1
Number of Residues33
DetailsRepeat: {"description":"TPR 1"}
ChainResidueDetails

site_idSWS_FT_FI2
Number of Residues33
DetailsRepeat: {"description":"TPR 2"}
ChainResidueDetails

site_idSWS_FT_FI3
Number of Residues33
DetailsRepeat: {"description":"TPR 3"}
ChainResidueDetails

site_idSWS_FT_FI4
Number of Residues32
DetailsRepeat: {"description":"TPR 4"}
ChainResidueDetails

site_idSWS_FT_FI5
Number of Residues32
DetailsRepeat: {"description":"TPR 5"}
ChainResidueDetails

site_idSWS_FT_FI6
Number of Residues32
DetailsRepeat: {"description":"TPR 6"}
ChainResidueDetails

site_idSWS_FT_FI7
Number of Residues33
DetailsRepeat: {"description":"TPR 7"}
ChainResidueDetails

site_idSWS_FT_FI8
Number of Residues33
DetailsRepeat: {"description":"TPR 8"}
ChainResidueDetails

site_idSWS_FT_FI9
Number of Residues32
DetailsRepeat: {"description":"TPR 9"}
ChainResidueDetails

site_idSWS_FT_FI10
Number of Residues35
DetailsRepeat: {"description":"TPR 10"}
ChainResidueDetails

site_idSWS_FT_FI11
Number of Residues236
DetailsRegion: {"description":"Interaction with PCM1","evidences":[{"source":"PubMed","id":"15107855","evidenceCode":"ECO:0000269"}]}
ChainResidueDetails

site_idSWS_FT_FI13
Number of Residues80
DetailsRegion: {"description":"Interaction with LZTL1","evidences":[{"source":"PubMed","id":"22072986","evidenceCode":"ECO:0000269"}]}
ChainResidueDetails

site_idSWS_FT_FI14
Number of Residues1
DetailsSite: {"description":"Critical for protein stability","evidences":[{"source":"PubMed","id":"26085087","evidenceCode":"ECO:0000269"}]}
ChainResidueDetails

247536

PDB entries from 2026-01-14

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