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4XZU

Crystal Structure of the Human Factor VIII C2 Domain in Complex with Murine 3E6 Inhibitory Antibody

Functional Information from PDB Data
site_idAC1
Number of Residues4
Detailsbinding site for residue MG A 301
ChainResidue
AVAL130
ACYS131
ATHR134
ATHR135

site_idAC2
Number of Residues2
Detailsbinding site for residue MG M 2401
ChainResidue
MTYR2195
MGLN2222

site_idAC3
Number of Residues3
Detailsbinding site for residue MG F 301
ChainResidue
FSER120
FSER121
FGLU122

Functional Information from PROSITE/UniProt
site_idPS00290
Number of Residues7
DetailsIG_MHC Immunoglobulins and major histocompatibility complex proteins signature. YTCEATH
ChainResidueDetails
BTYR191-HIS197

site_idPS01285
Number of Residues30
DetailsFA58C_1 Coagulation factors 5/8 type C domain (FA58C) signature 1. AWrpqvnnpke......WLqVDfqktmkVtgVtTQG
ChainResidueDetails
MALA2218-GLY2247

site_idPS01286
Number of Residues17
DetailsFA58C_2 Coagulation factors 5/8 type C domain (FA58C) signature 2. Pqswvhqia..LRmEVlGC
ChainResidueDetails
MPRO2310-CYS2326

Functional Information from SwissProt/UniProt
site_idSWS_FT_FI1
Number of Residues304
DetailsDomain: {"description":"F5/8 type C 2","evidences":[{"source":"PROSITE-ProRule","id":"PRU00081","evidenceCode":"ECO:0000255"}]}
ChainResidueDetails

244349

PDB entries from 2025-11-05

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