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PDB: 15 results
3T3L
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BU of 3t3l by Molmil
1.15 A structure of human frataxin variant Q153A
Descriptor: Frataxin, mitochondrial, SULFATE ION
Authors:Bridwell-Rabb, J, Winn, A.M, Barondeau, D.P.
Deposit date:2011-07-25
Release date:2011-08-10
Last modified:2024-02-28
Method:X-RAY DIFFRACTION (1.15 Å)
Cite:Structure-Function Analysis of Friedreich's Ataxia Mutants Reveals Determinants of Frataxin Binding and Activation of the Fe-S Assembly Complex.
Biochemistry, 50, 2011
3T3K
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1.24 A Structure of Friedreich's ataxia frataxin variant Q148R
Descriptor: Frataxin, mitochondrial
Authors:Bridwell-Rabb, J, Winn, A.M, Barondeau, D.P.
Deposit date:2011-07-25
Release date:2011-08-10
Last modified:2024-02-28
Method:X-RAY DIFFRACTION (1.24 Å)
Cite:Structure-Function Analysis of Friedreich's Ataxia Mutants Reveals Determinants of Frataxin Binding and Activation of the Fe-S Assembly Complex.
Biochemistry, 50, 2011
3S4M
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Crystal structure of wild-type human frataxin
Descriptor: Frataxin, mitochondrial
Authors:Tsai, C.-L, Bridwell-Rabb, J, Barondeau, D.P.
Deposit date:2011-05-19
Release date:2011-06-29
Last modified:2023-09-13
Method:X-RAY DIFFRACTION (1.3 Å)
Cite:Friedreich's Ataxia Variants I154F and W155R Diminish Frataxin-Based Activation of the Iron-Sulfur Cluster Assembly Complex.
Biochemistry, 50, 2011
3S5E
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Crystal structure of human frataxin variant W155R, one of the Friedreich's ataxia point mutations
Descriptor: Frataxin, mitochondrial, MAGNESIUM ION
Authors:Tsai, C.-L, Bridwell-Rabb, J, Barondeau, D.P.
Deposit date:2011-05-23
Release date:2011-06-29
Last modified:2023-09-13
Method:X-RAY DIFFRACTION (1.31 Å)
Cite:Friedreich's Ataxia Variants I154F and W155R Diminish Frataxin-Based Activation of the Iron-Sulfur Cluster Assembly Complex.
Biochemistry, 50, 2011
3T3T
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1.38 A structure of human frataxin variant Q148G
Descriptor: Frataxin, mitochondrial, SULFATE ION
Authors:Bridwell-Rabb, J, Winn, A.M, Barondeau, D.P.
Deposit date:2011-07-25
Release date:2011-08-10
Last modified:2024-02-28
Method:X-RAY DIFFRACTION (1.38 Å)
Cite:Structure-Function Analysis of Friedreich's Ataxia Mutants Reveals Determinants of Frataxin Binding and Activation of the Fe-S Assembly Complex.
Biochemistry, 50, 2011
3S5F
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BU of 3s5f by Molmil
Crystal structure of human frataxin variant W155F
Descriptor: Frataxin, mitochondrial, MAGNESIUM ION
Authors:Tsai, C.-L, Bridwell-Rabb, J, Barondeau, D.P.
Deposit date:2011-05-23
Release date:2011-06-29
Last modified:2023-09-13
Method:X-RAY DIFFRACTION (1.5 Å)
Cite:Friedreich's Ataxia Variants I154F and W155R Diminish Frataxin-Based Activation of the Iron-Sulfur Cluster Assembly Complex.
Biochemistry, 50, 2011
3S5D
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BU of 3s5d by Molmil
Crystal structure of human frataxin variant W155A
Descriptor: Frataxin, mitochondrial, SULFATE ION
Authors:Tsai, C.-L, Bridwell-Rabb, J, Barondeau, D.P.
Deposit date:2011-05-23
Release date:2011-06-29
Last modified:2023-09-13
Method:X-RAY DIFFRACTION (1.5 Å)
Cite:Friedreich's Ataxia Variants I154F and W155R Diminish Frataxin-Based Activation of the Iron-Sulfur Cluster Assembly Complex.
Biochemistry, 50, 2011
3T3X
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BU of 3t3x by Molmil
1.57 A structure of Friedreich's ataxia frataxin variant R165C
Descriptor: Frataxin, mitochondrial, SULFATE ION
Authors:Bridwell-Rabb, J, Winn, A.M, Barondeau, D.P.
Deposit date:2011-07-25
Release date:2011-08-10
Last modified:2024-02-28
Method:X-RAY DIFFRACTION (1.57 Å)
Cite:Structure-Function Analysis of Friedreich's Ataxia Mutants Reveals Determinants of Frataxin Binding and Activation of the Fe-S Assembly Complex.
Biochemistry, 50, 2011
3T3J
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BU of 3t3j by Molmil
1.70 A structure of Friedreich's ataxia frataxin variant N146K
Descriptor: Frataxin, mitochondrial
Authors:Bridwell-Rabb, J, Winn, A.M, Barondeau, D.P.
Deposit date:2011-07-25
Release date:2011-08-10
Last modified:2024-02-28
Method:X-RAY DIFFRACTION (1.7 Å)
Cite:Structure-Function Analysis of Friedreich's Ataxia Mutants Reveals Determinants of Frataxin Binding and Activation of the Fe-S Assembly Complex.
Biochemistry, 50, 2011
1EKG
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BU of 1ekg by Molmil
MATURE HUMAN FRATAXIN
Descriptor: FRATAXIN
Authors:Dhe-Paganon, S, Shigeta, R, Chi, Y.I, Ristow, M, Shoelson, S.E.
Deposit date:2000-03-08
Release date:2000-11-08
Last modified:2024-02-07
Method:X-RAY DIFFRACTION (1.8 Å)
Cite:Crystal structure of human frataxin.
J.Biol.Chem., 275, 2000
8PK8
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BU of 8pk8 by Molmil
Structure of the human mitochondrial iron-sulfur cluster biosynthesis complex during persulfide transfer (persulfide on ISCU2)
Descriptor: Acyl carrier protein, Cysteine desulfurase, FE (II) ION, ...
Authors:Steinhilper, R, Murphy, B.J.
Deposit date:2023-06-26
Release date:2024-05-01
Method:ELECTRON MICROSCOPY (2.49 Å)
Cite:Mechanism and structural dynamics of sulfur transfer during de novo [2Fe-2S] cluster assembly on ISCU2.
Nat Commun, 15, 2024
8PK9
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BU of 8pk9 by Molmil
Structure of the human mitochondrial iron-sulfur cluster biosynthesis complex during persulfide transfer (persulfide on NFS1 and ISCU2)
Descriptor: Acyl carrier protein, Cysteine desulfurase, FE (II) ION, ...
Authors:Steinhilper, R, Murphy, B.J.
Deposit date:2023-06-26
Release date:2024-05-01
Method:ELECTRON MICROSCOPY (2.58 Å)
Cite:Mechanism and structural dynamics of sulfur transfer during de novo [2Fe-2S] cluster assembly on ISCU2.
Nat Commun, 15, 2024
6NZU
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BU of 6nzu by Molmil
Structure of the human frataxin-bound iron-sulfur cluster assembly complex
Descriptor: Acyl carrier protein, Cysteine desulfurase, mitochondrial, ...
Authors:Fox, N.G, Yu, X, Xidong, F, Alain, M, Joseph, N, Claire, S.D, Christine, B, Han, S, Yue, W.W.
Deposit date:2019-02-14
Release date:2019-05-22
Last modified:2019-07-10
Method:ELECTRON MICROSCOPY (3.2 Å)
Cite:Structure of the human frataxin-bound iron-sulfur cluster assembly complex provides insight into its activation mechanism.
Nat Commun, 10, 2019
5KZ5
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BU of 5kz5 by Molmil
Architecture of the Human Mitochondrial Iron-Sulfur Cluster Assembly Machinery: the Complex Formed by the Iron Donor, the Sulfur Donor, and the Scaffold
Descriptor: Cysteine desulfurase, mitochondrial, Frataxin, ...
Authors:Gakh, O, Ranatunga, W, Smith, D.Y, Ahlgren, E.C, Al-Karadaghi, S, Thompson, J.R, Isaya, G.
Deposit date:2016-07-22
Release date:2016-08-31
Last modified:2024-10-23
Method:ELECTRON MICROSCOPY (14.3 Å)
Cite:Architecture of the Human Mitochondrial Iron-Sulfur Cluster Assembly Machinery.
J.Biol.Chem., 291, 2016
1LY7
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BU of 1ly7 by Molmil
The solution structure of the the c-terminal domain of frataxin, the protein responsible for friedreich ataxia
Descriptor: frataxin
Authors:Musco, G, Stier, G, Kolmerer, B, Adinolfi, S, Martin, S, Frenkiel, T, Gibson, T, Pastore, A.
Deposit date:2002-06-07
Release date:2002-06-26
Last modified:2024-05-22
Method:SOLUTION NMR
Cite:Towards a structural understanding of Friedreich's ataxia: the solution structure of frataxin
Structure Fold.Des., 8, 2000

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PDB entries from 2024-11-06

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