6Z9U
Crystal structure of a TSEN15-34 heterodimer.
Summary for 6Z9U
Entry DOI | 10.2210/pdb6z9u/pdb |
Descriptor | tRNA-splicing endonuclease subunit Sen34, tRNA-splicing endonuclease subunit Sen15, GLYCEROL, ... (4 entities in total) |
Functional Keywords | trna splicing endonuclease, tsen, precursor trna, pre-trna processing, neurodegenerative disorders, pontocerebellar hypoplasia, splicing |
Biological source | Homo sapiens (Human) More |
Total number of polymer chains | 4 |
Total formula weight | 61201.40 |
Authors | Trowitzsch, S.,Sekulovski, S. (deposition date: 2020-06-04, release date: 2021-06-30, Last modification date: 2024-01-24) |
Primary citation | Sekulovski, S.,Devant, P.,Panizza, S.,Gogakos, T.,Pitiriciu, A.,Heitmeier, K.,Ramsay, E.P.,Barth, M.,Schmidt, C.,Tuschl, T.,Baas, F.,Weitzer, S.,Martinez, J.,Trowitzsch, S. Assembly defects of human tRNA splicing endonuclease contribute to impaired pre-tRNA processing in pontocerebellar hypoplasia. Nat Commun, 12:5610-5610, 2021 Cited by PubMed: 34584079DOI: 10.1038/s41467-021-25870-3 PDB entries with the same primary citation |
Experimental method | X-RAY DIFFRACTION (2.10001777636 Å) |
Structure validation
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