6SDZ
transthyritin derived amyloid fibril from patient with hereditary V30M ATTR amyloidosis
Summary for 6SDZ
Entry DOI | 10.2210/pdb6sdz/pdb |
EMDB information | 10150 |
Descriptor | Transthyretin (1 entity in total) |
Functional Keywords | amyloid fibril, systemic attr amyloidosis, ex vivo, misfolding, patient tissue, transthyritin, protein fibril |
Biological source | Homo sapiens (Human) |
Total number of polymer chains | 11 |
Total formula weight | 151903.69 |
Authors | Fritz, G.,Agarwal, S.,Faendrich, M. (deposition date: 2019-07-29, release date: 2019-11-13, Last modification date: 2024-05-22) |
Primary citation | Schmidt, M.,Wiese, S.,Adak, V.,Engler, J.,Agarwal, S.,Fritz, G.,Westermark, P.,Zacharias, M.,Fandrich, M. Cryo-EM structure of a transthyretin-derived amyloid fibril from a patient with hereditary ATTR amyloidosis. Nat Commun, 10:5008-5008, 2019 Cited by PubMed: 31676763DOI: 10.1038/s41467-019-13038-z PDB entries with the same primary citation |
Experimental method | ELECTRON MICROSCOPY (2.97 Å) |
Structure validation
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