3GXM
Crystal structure of acid-beta-glucosidase at pH 4.5, phosphate crystallization condition
Summary for 3GXM
Entry DOI | 10.2210/pdb3gxm/pdb |
Related | 3GXF 3GXI |
Descriptor | Glucosylceramidase, 2-acetamido-2-deoxy-beta-D-glucopyranose, SULFATE ION, ... (4 entities in total) |
Functional Keywords | hydrolase, alternative initiation, disease mutation, disulfide bond, gaucher disease, glycoprotein, glycosidase, ichthyosis, lipid metabolism, lysosome, membrane, sphingolipid metabolism |
Biological source | Homo sapiens (human) |
Total number of polymer chains | 4 |
Total formula weight | 226135.27 |
Authors | Lieberman, R.L. (deposition date: 2009-04-02, release date: 2009-05-05, Last modification date: 2020-07-29) |
Primary citation | Lieberman, R.L.,D'aquino, J.A.,Ringe, D.,Petsko, G.A. Effects of pH and iminosugar pharmacological chaperones on lysosomal glycosidase structure and stability. Biochemistry, 48:4816-4827, 2009 Cited by PubMed: 19374450DOI: 10.1021/bi9002265 PDB entries with the same primary citation |
Experimental method | X-RAY DIFFRACTION (2.2 Å) |
Structure validation
Download full validation report