3GXF
Crystal structure of acid-beta-glucosidase with isofagomine at neutral pH
Summary for 3GXF
Entry DOI | 10.2210/pdb3gxf/pdb |
Related | 3GXI 3GXM |
Descriptor | Glucosylceramidase, PHOSPHATE ION, 2-acetamido-2-deoxy-beta-D-glucopyranose, ... (6 entities in total) |
Functional Keywords | hydrolase, alternative initiation, disease mutation, disulfide bond, gaucher disease, glycoprotein, glycosidase, ichthyosis, lipid metabolism, lysosome, membrane, sphingolipid metabolism |
Biological source | Homo sapiens (human) |
Total number of polymer chains | 4 |
Total formula weight | 230278.46 |
Authors | Lieberman, R.L. (deposition date: 2009-04-02, release date: 2009-05-05, Last modification date: 2023-09-06) |
Primary citation | Lieberman, R.L.,D'aquino, J.A.,Ringe, D.,Petsko, G.A. Effects of pH and iminosugar pharmacological chaperones on lysosomal glycosidase structure and stability. Biochemistry, 48:4816-4827, 2009 Cited by PubMed: 19374450DOI: 10.1021/bi9002265 PDB entries with the same primary citation |
Experimental method | X-RAY DIFFRACTION (2.4 Å) |
Structure validation
Download full validation report