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8JXN

Human 3-methylcrotonyl-CoA carboxylase in BCCP-H1 state with MCoA

Entity
Entity IDChain IDDescriptionTypeChain lengthFormula weightNumber of moleculesDB Name (Accession)Biological sourceDescriptive keywords
1A, D, G, J, K...
(D, G, I, B, K...)
Methylcrotonoyl-CoA carboxylase beta chain, mitochondrialpolymer56361406.06UniProt (Q9HCC0)
Pfam (PF01039)
Homo sapiens (human)MCCase subunit beta,3-methylcrotonyl-CoA carboxylase 2,3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit,3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta
2B, C, E, F, H...
(E, F, H, C, J...)
Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrialpolymer72580584.06UniProt (Q96RQ3)
Pfam (PF00289)
Pfam (PF02786)
Pfam (PF02785)
Pfam (PF00364)
Homo sapiens (human)MCCase subunit alpha,3-methylcrotonyl-CoA carboxylase 1,3-methylcrotonyl-CoA carboxylase biotin-containing subunit,3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha
3M, O, P, Q, T...
(D, E, F, G, I...)
5-(HEXAHYDRO-2-OXO-1H-THIENO[3,4-D]IMIDAZOL-6-YL)PENTANALnon-polymer228.36Chemie (BTI)
4N, R, S, V, W...
(D, G, I, B, K...)
~{S}-[2-[3-[[(2~{R})-4-[[[(2~{S},3~{S},4~{S},5~{S})-5-(6-aminopurin-9-yl)-4-oxidanyl-3-phosphonooxy-oxolan-2-yl]methoxy-oxidanyl-phosphoryl]oxy-oxidanyl-phosphoryl]oxy-3,3-dimethyl-2-oxidanyl-butanoyl]amino]propanoylamino]ethyl] 3-methylbut-2-enethioatenon-polymer849.66Chemie (TW3)
Sequence viewer
Contents of the asymmetric unit
PolymersNumber of chains12
Total formula weight851940.3
Non-Polymers*Number of molecules12
Total formula weight6467.7
All*Total formula weight858407.9
*Water molecules are not included.

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PDB entries from 2026-01-21

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