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7UN5

Structure of Type II Prion filaments from Gerstmann-Straussler-Scheinker disease

Entity
Entity IDChain IDDescriptionTypeChain lengthFormula weightNumber of moleculesDB Name (Accession)Biological sourceDescriptive keywords
1A, B, C, D, E...
(E, A, B, C, D...)
Major prion proteinpolymer626219.010UniProt (P04156)Homo sapiens (human)PrP,ASCR,PrP27-30,PrP33-35C
Sequence modifications
E, A, B, C, D, H, F, G, I, J: 80 - 141 (UniProt: P04156)
PDBExternal DatabaseDetails
Val 129Met 129variant
Sequence viewer
Contents of the asymmetric unit
PolymersNumber of chains10
Total formula weight62190.4
All*Total formula weight62190.4
*Water molecules are not included.

247536

PDB entries from 2026-01-14

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