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6TJJ

Structure of Cerezyme at pH 4.6

This is a non-PDB format compatible entry.
Entity
Entity IDChain IDDescriptionTypeChain lengthFormula weightNumber of moleculesDB Name (Accession)Biological sourceDescriptive keywords
1A, B
(AAA, BBB)
Glucosylceramidasepolymer49755640.22UniProt (P04062)
Pfam (PF02055)
Pfam (PF17189)
Homo sapiens (Human)Acid beta-glucosidase,Alglucerase,Beta-glucocerebrosidase,Beta-GC,D-glucosyl-N-acylsphingosine glucohydrolase,Imiglucerase
2C, D
(A, B)
2-acetamido-2-deoxy-beta-D-glucopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranosebranched424.42In PDB
GlyTouCan (G42666HT)
3AA, BA, DA, E, F...
(BBB, AAA)
SULFATE IONnon-polymer96.118Chemie (SO4)
4CA, EA, GA, HA, IA...
(BBB, AAA)
ACETATE IONnon-polymer59.016Chemie (ACT)
5FA, W
(BBB, AAA)
2-acetamido-2-deoxy-beta-D-glucopyranosenon-polymer221.22Chemie (NAG)
6OA
(BBB)
POTASSIUM IONnon-polymer39.11Chemie (K)
7PA
(BBB)
SODIUM IONnon-polymer23.01Chemie (NA)
8QA, RA
(AAA, BBB)
waterwater18.0715Chemie (HOH)
Sequence modifications
AAA, BBB: 1 - 497 (UniProt: P04062)
PDBExternal DatabaseDetails
His 495Arg 534conflict
Sequence viewer
Contents of the asymmetric unit
PolymersNumber of chains2
Total formula weight111280.3
BranchedNumber of molecules2
Total formula weight848.8
Non-Polymers*Number of molecules38
Total formula weight3178.3
All*Total formula weight115307.5
*Water molecules are not included.

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PDB entries from 2025-12-03

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