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5XTH

Cryo-EM structure of human respiratory supercomplex I1III2IV1

This is a non-PDB format compatible entry.
Entity
Entity IDChain IDDescriptionTypeChain lengthFormula weightNumber of moleculesDB Name (Accession)Biological sourceDescriptive keywords
1ANADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrialpolymer43147323.91UniProt (P49821)
Pfam (PF01512)
Pfam (PF10589)
In PDB
Homo sapiens (Human)Complex I-51kD,CI-51kD,NADH dehydrogenase flavoprotein 1,NADH-ubiquinone oxidoreductase 51 kDa subunit
2BNADH dehydrogenase [ubiquinone] iron-sulfur protein 8, mitochondrialpolymer17620314.01UniProt (O00217)
Pfam (PF12838)
In PDB
Homo sapiens (Human)Complex I-23kD,CI-23kD,NADH-ubiquinone oxidoreductase 23 kDa subunit,TYKY subunit
3CNADH dehydrogenase [ubiquinone] iron-sulfur protein 7, mitochondrialpolymer15617887.91UniProt (O75251)
Pfam (PF01058)
In PDB
Homo sapiens (Human)Complex I-20kD,CI-20kD,NADH-ubiquinone oxidoreductase 20 kDa subunit,PSST subunit
4ENADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 6polymer11313758.11UniProt (P56556)
Pfam (PF13233)
In PDB
Homo sapiens (Human)Complex I-B14,CI-B14,LYR motif-containing protein 6,NADH-ubiquinone oxidoreductase B14 subunit
5FNADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 2polymer839535.91UniProt (O43678)
Pfam (PF05047)
In PDB
Homo sapiens (Human)Complex I-B8,CI-B8,NADH-ubiquinone oxidoreductase B8 subunit
6G, XAcyl carrier protein, mitochondrialpolymer859845.22UniProt (O14561)
Pfam (PF00550)
In PDB
Homo sapiens (Human)ACP,CI-SDAP,NADH-ubiquinone oxidoreductase 9.6 kDa subunit
7HNADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 5polymer11213119.21UniProt (Q16718)
Pfam (PF04716)
In PDB
Homo sapiens (Human)Complex I subunit B13,Complex I-13kD-B,CI-13kD-B,NADH-ubiquinone oxidoreductase 13 kDa-B subunit
8INADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 7polymer11012282.11UniProt (O95182)
Pfam (PF07347)
In PDB
Homo sapiens (Human)Complex I-B14.5a,CI-B14.5a,NADH-ubiquinone oxidoreductase subunit B14.5a
9JNADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 9, mitochondrialpolymer33738387.61UniProt (Q16795)
Pfam (PF01370)
In PDB
Homo sapiens (Human)Complex I-39kD,CI-39kD,NADH-ubiquinone oxidoreductase 39 kDa subunit
10KNADH dehydrogenase [ubiquinone] flavoprotein 3, mitochondrialpolymer333900.31UniProt (P56181)
Pfam (PF15880)
In PDB
Homo sapiens (Human)Complex I-9kD,CI-9kD,NADH-ubiquinone oxidoreductase 9 kDa subunit,Renal carcinoma antigen NY-REN-4
11LNADH dehydrogenase [ubiquinone] iron-sulfur protein 4, mitochondrialpolymer11813721.61UniProt (O43181)
Pfam (PF04800)
In PDB
Homo sapiens (Human)Complex I-18 kDa,CI-18 kDa,Complex I-AQDQ,CI-AQDQ,NADH-ubiquinone oxidoreductase 18 kDa subunit
12MNADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrialpolymer68775471.51UniProt (P28331)
Pfam (PF13510)
Pfam (PF10588)
Pfam (PF00384)
Pfam (PF09326)
In PDB
Homo sapiens (Human)Complex I-75kD,CI-75kD
13NNADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 12polymer14316880.11UniProt (Q9UI09)
Pfam (PF05071)
In PDB
Homo sapiens (Human)13 kDa differentiation-associated protein,Complex I-B17.2,CIB17.2,NADH-ubiquinone oxidoreductase subunit B17.2
14ONADH dehydrogenase [ubiquinone] flavoprotein 2, mitochondrialpolymer21223430.91UniProt (P19404)
Pfam (PF01257)
In PDB
Homo sapiens (Human)NADH-ubiquinone oxidoreductase 24 kDa subunit
15PNADH dehydrogenase [ubiquinone] iron-sulfur protein 3, mitochondrialpolymer20824432.71UniProt (O75489)
Pfam (PF00329)
In PDB
Homo sapiens (Human)Complex I-30kD,CI-30kD,NADH-ubiquinone oxidoreductase 30 kDa subunit
16QNADH dehydrogenase [ubiquinone] iron-sulfur protein 2, mitochondrialpolymer43049236.51UniProt (O75306)
Pfam (PF00346)
In PDB
Homo sapiens (Human)Complex I-49kD,CI-49kD,NADH-ubiquinone oxidoreductase 49 kDa subunit
17SNADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1polymer708084.41UniProt (O15239)
Pfam (PF15879)
In PDB
Homo sapiens (Human)Complex I-MWFE,CI-MWFE,NADH-ubiquinone oxidoreductase MWFE subunit
18TNADH dehydrogenase [ubiquinone] iron-sulfur protein 6, mitochondrialpolymer9510578.81UniProt (O75380)
Pfam (PF10276)
In PDB
Homo sapiens (Human)Complex I-13kD-A,CI-13kD-A,NADH-ubiquinone oxidoreductase 13 kDa-A subunit
19UNADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 3polymer839156.61UniProt (O95167)
Pfam (PF14987)
In PDB
Homo sapiens (Human)Complex I-B9,CI-B9,NADH-ubiquinone oxidoreductase B9 subunit
20VNADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 11polymer14014736.91UniProt (Q86Y39)
In PDB
Homo sapiens (Human)Complex I-B14.7,CI-B14.7,NADH-ubiquinone oxidoreductase subunit B14.7
21WNADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 13polymer13816132.61UniProt (Q9P0J0)
Pfam (PF06212)
In PDB
Homo sapiens (Human)Cell death regulatory protein GRIM-19,Complex I-B16.6,CI-B16.6,Gene associated with retinoic and interferon-induced mortality 19 protein,Gene associated with retinoic and IFN-induced mortality 19 protein,NADH-ubiquinone oxidoreductase B16.6 subunit
22YNADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 2, mitochondrialpolymer597468.31UniProt (O95178)
Pfam (PF14813)
In PDB
Homo sapiens (Human)Complex I-AGGG,CI-AGGG,NADH-ubiquinone oxidoreductase AGGG subunit
23ZNADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 3polymer809261.61UniProt (O43676)
Pfam (PF08122)
In PDB
Homo sapiens (Human)Complex I-B12,CI-B12,NADH-ubiquinone oxidoreductase B12 subunit
24aNADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 5, mitochondrialpolymer13816573.21UniProt (O43674)
Pfam (PF09781)
In PDB
Homo sapiens (Human)Complex I-SGDH,CI-SGDH,NADH-ubiquinone oxidoreductase SGDH subunit
25bNADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 6polymer12415008.61UniProt (O95139)
Pfam (PF09782)
In PDB
Homo sapiens (Human)Complex I-B17,CI-B17,NADH-ubiquinone oxidoreductase B17 subunit
26cNADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 8, mitochondrialpolymer15318267.61UniProt (O95169)
Pfam (PF05821)
In PDB
Homo sapiens (Human)Complex I-ASHI,CI-ASHI,NADH-ubiquinone oxidoreductase ASHI subunit
27dNADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 10polymer17120721.71UniProt (O96000)
Pfam (PF10249)
In PDB
Homo sapiens (Human)Complex I-PDSW,CI-PDSW,NADH-ubiquinone oxidoreductase PDSW subunit
28eNADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 11, mitochondrialpolymer9711494.91UniProt (Q9NX14)
Pfam (PF10183)
In PDB
Homo sapiens (Human)Complex I-ESSS,CI-ESSS,NADH-ubiquinone oxidoreductase ESSS subunit,Neuronal protein 17.3,p17.3
29fNADH dehydrogenase [ubiquinone] 1 subunit C1, mitochondrialpolymer475704.61UniProt (O43677)
Pfam (PF15088)
In PDB
Homo sapiens (Human)Complex I-KFYI,CI-KFYI,NADH-ubiquinone oxidoreductase KFYI subunit
30gNADH dehydrogenase [ubiquinone] 1 subunit C2polymer11914209.51UniProt (O95298)
Pfam (PF06374)
In PDB
Homo sapiens (Human)Complex I-B14.5b,CI-B14.5b,Human lung cancer oncogene 1 protein,HLC-1,NADH-ubiquinone oxidoreductase subunit B14.5b
31hNADH dehydrogenase [ubiquinone] iron-sulfur protein 5polymer10412314.31UniProt (O43920)
Pfam (PF10200)
In PDB
Homo sapiens (Human)Complex I-15 kDa,CI-15 kDa,NADH-ubiquinone oxidoreductase 15 kDa subunit
32iNADH-ubiquinone oxidoreductase chain 2polymer34739007.71UniProt (Q4GRX1)
Pfam (PF00361)
Pfam (PF06444)
UniProt (by SIFTS) (P03891)
In PDB
Homo sapiens (Human)
33jNADH-ubiquinone oxidoreductase chain 3polymer11513147.91UniProt (B9EE38)
Pfam (PF00507)
In PDB
Homo sapiens (Human)
34kNADH-ubiquinone oxidoreductase chain 4Lpolymer9710702.11UniProt (V9JN72)
Pfam (PF00420)
In PDB
Homo sapiens (Human)
35lNADH-ubiquinone oxidoreductase chain 5polymer60367096.01UniProt (X5BVZ3)
Pfam (PF00662)
Pfam (PF00361)
Pfam (PF06455)
UniProt (by SIFTS) (P03915)
In PDB
Homo sapiens (Human)
36mNADH-ubiquinone oxidoreductase chain 6polymer17418661.01UniProt (Q8HAX7)
Pfam (PF00499)
In PDB
Homo sapiens (Human)
37nNADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 1polymer566741.91UniProt (O75438)
Pfam (PF08040)
In PDB
Homo sapiens (Human)Complex I-MNLL,CI-MNLL,NADH-ubiquinone oxidoreductase MNLL subunit
38oNADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 4polymer12815100.41UniProt (O95168)
Pfam (PF07225)
In PDB
Homo sapiens (Human)Complex I-B15,CI-B15,NADH-ubiquinone oxidoreductase B15 subunit
39pNADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 9polymer17221189.11UniProt (Q9Y6M9)
Pfam (PF05347)
In PDB
Homo sapiens (Human)Complex I-B22,CI-B22,LYR motif-containing protein 3,NADH-ubiquinone oxidoreductase B22 subunit
40rNADH-ubiquinone oxidoreductase chain 4polymer45951689.71UniProt (B2XJG5)
Pfam (PF01059)
Pfam (PF00361)
UniProt (by SIFTS) (P03905)
In PDB
Homo sapiens (Human)
41sNADH-ubiquinone oxidoreductase chain 1polymer31835621.21UniProt (H9PGF0)
Pfam (PF00146)
In PDB
Homo sapiens (Human)
42uNADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 8polymer16919853.71UniProt (P51970)
Pfam (PF06747)
In PDB
Homo sapiens (Human)Complex I-19kD,CI-19kD,Complex I-PGIV,CI-PGIV,NADH-ubiquinone oxidoreductase 19 kDa subunit
43vNADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 7polymer12214997.41UniProt (P17568)
Pfam (PF05676)
In PDB
Homo sapiens (Human)Cell adhesion protein SQM1,Complex I-B18,CI-B18,NADH-ubiquinone oxidoreductase B18 subunit
44wNADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 10, mitochondrialpolymer32037200.31UniProt (O95299)
Pfam (PF01712)
In PDB
Homo sapiens (Human)Complex I-42kD,CI-42kD,NADH-ubiquinone oxidoreductase 42 kDa subunit
45xCytochrome c oxidase subunit 1polymer51457065.81UniProt (P00396)
Pfam (PF00115)
In PDB
Bos taurus (Bovine)Cytochrome c oxidase polypeptide I
46yCytochrome c oxidase subunit 2polymer22726040.41UniProt (P68530)
Pfam (PF02790)
Pfam (PF00116)
In PDB
Bos taurus (Bovine)Cytochrome c oxidase polypeptide II
47zCytochrome c oxidase subunit 3polymer26129957.61UniProt (P00415)
Pfam (PF00510)
In PDB
Bos taurus (Bovine)Cytochrome c oxidase polypeptide III
480Cytochrome c oxidase subunit 4 isoform 1, mitochondrialpolymer14416913.41UniProt (P00423)
Pfam (PF02936)
In PDB
Bos taurus (Bovine)Cytochrome c oxidase polypeptide IV,Cytochrome c oxidase subunit IV isoform 1,COX IV-1
491Cytochrome c oxidase subunit 5A, mitochondrialpolymer10912453.11UniProt (P00426)
Pfam (PF02284)
In PDB
Bos taurus (Bovine)Cytochrome c oxidase polypeptide Va
502Cytochrome c oxidase subunit 5B, mitochondrialpolymer9810684.01UniProt (P00428)
Pfam (PF01215)
In PDB
Bos taurus (Bovine)Cytochrome c oxidase polypeptide VIa,Cytochrome c oxidase polypeptide Vb
513Cytochrome c oxidase subunit 6A2, mitochondrialpolymer849452.71UniProt (P07471)
Pfam (PF02046)
In PDB
Bos taurus (Bovine)Cytochrome c oxidase polypeptide VIa-heart,COXVIAH,Cytochrome c oxidase polypeptide VIb
524Cytochrome c oxidase subunit 6B1polymer758926.01UniProt (P00429)
Pfam (PF02297)
In PDB
Bos taurus (Bovine)Cytochrome c oxidase polypeptide VII,Cytochrome c oxidase subunit AED,Cytochrome c oxidase subunit VIb isoform 1,COX VIb-1
535Cytochrome c oxidase subunit 6Cpolymer738495.01UniProt (P04038)
Pfam (PF02937)
In PDB
Bos taurus (Bovine)Cytochrome c oxidase polypeptide VIc,Cytochrome c oxidase subunit STA
546Cytochrome c oxidase subunit 7A1, mitochondrialpolymer566286.21UniProt (P07470)
Pfam (PF02238)
In PDB
Bos taurus (Bovine)Cytochrome c oxidase subunit VIIIc,VIIIC,Cytochrome c oxidase subunit VIIa-heart,Cytochrome c oxidase subunit VIIa-H,Cytochrome c oxidase subunit VIIa-muscle,Cytochrome c oxidase subunit VIIa-M
557Cytochrome c oxidase subunit 7B, mitochondrialpolymer495442.21UniProt (P13183)
Pfam (PF05392)
In PDB
Bos taurus (Bovine)Cytochrome c oxidase polypeptide VIIb,IHQ
568Cytochrome c oxidase subunit 7C, mitochondrialpolymer475449.41UniProt (P00430)
Pfam (PF02935)
In PDB
Bos taurus (Bovine)Cytochrome c oxidase polypeptide VIIIA,Cytochrome c oxidase polypeptide VIIc
579Cytochrome c oxidase subunit 8B, mitochondrialpolymer434738.51UniProt (P10175)
Pfam (PF02285)
In PDB
Bos taurus (Bovine)Cytochrome c oxidase polypeptide VIII-heart,Cytochrome c oxidase subunit 8-1,Cytochrome c oxidase subunit 8H,IX,VIIIb
58AA, ANCytochrome b-c1 complex subunit 8polymer819791.22UniProt (O14949)
Pfam (PF02939)
In PDB
Homo sapiens (Human)Complex III subunit 8,Complex III subunit VIII,Ubiquinol-cytochrome c reductase complex 9.5 kDa protein,Ubiquinol-cytochrome c reductase complex ubiquinone-binding protein QP-C
59AB, AOCytochrome b-c1 complex subunit Rieske, mitochondrialpolymer575893.82UniProt (P47985)
Pfam (PF09165)
In PDB
Homo sapiens (Human)Complex III subunit 5,Cytochrome b-c1 complex subunit 5,Rieske iron-sulfur protein,RISP,Ubiquinol-cytochrome c reductase iron-sulfur subunit
60AC, APCytochrome b-c1 complex subunit Rieske, mitochondrialpolymer19621645.62UniProt (P47985)
Pfam (PF02921)
Pfam (PF00355)
In PDB
Homo sapiens (Human)Complex III subunit 5,Cytochrome b-c1 complex subunit 5,Rieske iron-sulfur protein,RISP,Ubiquinol-cytochrome c reductase iron-sulfur subunit
61AD, AQCytochrome b-c1 complex subunit 9polymer627189.32UniProt (Q9UDW1)
Pfam (PF05365)
In PDB
Homo sapiens (Human)Complex III subunit 9,Complex III subunit X,Cytochrome c1 non-heme 7 kDa protein,Ubiquinol-cytochrome c reductase complex 7.2 kDa protein
62AE, ARCytochrome b-c1 complex subunit 6, mitochondrialpolymer748861.72UniProt (P07919)
Pfam (PF02320)
In PDB
Homo sapiens (Human)Complex III subunit 6,Complex III subunit VIII,Cytochrome c1 non-heme 11 kDa protein,Mitochondrial hinge protein,Ubiquinol-cytochrome c reductase complex 11 kDa protein
63AF, ASCytochrome b-c1 complex subunit 7polymer10613037.82UniProt (P14927)
Pfam (PF02271)
In PDB
Homo sapiens (Human)Complex III subunit 7,Complex III subunit VII,QP-C,Ubiquinol-cytochrome c reductase complex 14 kDa protein
64AG, ATCytochrome b-c1 complex subunit 10polymer515958.92UniProt (O14957)
Pfam (PF08997)
In PDB
Homo sapiens (Human)Complex III subunit 10,Complex III subunit XI,Ubiquinol-cytochrome c reductase complex 6.4 kDa protein
65AH, AUCytochrome c1, heme protein, mitochondrialpolymer24127388.42UniProt (P08574)
Pfam (PF02167)
In PDB
Homo sapiens (Human)Complex III subunit 4,Complex III subunit IV,Cytochrome b-c1 complex subunit 4,Ubiquinol-cytochrome-c reductase complex cytochrome c1 subunit,Cytochrome c-1
66AJ, AVCytochrome bpolymer37842543.02UniProt (P00156)
Pfam (PF00033)
Pfam (PF00032)
In PDB
Homo sapiens (Human)Complex III subunit 3,Complex III subunit III,Cytochrome b-c1 complex subunit 3,Ubiquinol-cytochrome-c reductase complex cytochrome b subunit
67AK, AWCytochrome b-c1 complex subunit 2, mitochondrialpolymer41944946.62UniProt (P22695)
Pfam (PF00675)
Pfam (PF05193)
In PDB
Homo sapiens (Human)Complex III subunit 2,Core protein II,Ubiquinol-cytochrome-c reductase complex core protein 2
68AL, AYCytochrome b-c1 complex subunit 1, mitochondrialpolymer44649181.42UniProt (P31930)
Pfam (PF00675)
Pfam (PF05193)
In PDB
Homo sapiens (Human)Complex III subunit 1,Core protein I,Ubiquinol-cytochrome-c reductase complex core protein 1
69A, B, C, MIRON/SULFUR CLUSTERnon-polymer351.66Chemie (SF4)
70AFLAVIN MONONUCLEOTIDEnon-polymer456.31Chemie (FMN)
71AQ, r, AT, B, U...(9R,11S)-9-({[(1S)-1-HYDROXYHEXADECYL]OXY}METHYL)-2,2-DIMETHYL-5,7,10-TRIOXA-2LAMBDA~5~-AZA-6LAMBDA~5~-PHOSPHAOCTACOSANE-6,6,11-TRIOLnon-polymer767.112Chemie (PLX)
72p, ES-[2-({N-[(2R)-2-hydroxy-3,3-dimethyl-4-(phosphonooxy)butanoyl]-beta-alanyl}amino)ethyl] dodecanethioatenon-polymer540.72Chemie (8Q1)
73JNADPH DIHYDRO-NICOTINAMIDE-ADENINE-DINUCLEOTIDE PHOSPHATEnon-polymer745.41Chemie (NDP)
74AP, M, O, ACFE2/S2 (INORGANIC) CLUSTERnon-polymer175.84Chemie (FES)
75l, AN, n, AU, AY...CARDIOLIPINnon-polymer1464.014Chemie (CDL)
76AL, AU, AV, AY, V...1,2-Dioleoyl-sn-glycero-3-phosphoethanolaminenon-polymer749.110Chemie (PEE)
77x, yCOPPER (II) IONnon-polymer63.53Chemie (CU)
78xMAGNESIUM IONnon-polymer24.31Chemie (MG)
79xHEME-Anon-polymer852.82Chemie (HEA)
802ZINC IONnon-polymer65.41Chemie (ZN)
81AU, AHHEME Cnon-polymer618.52Chemie (HEC)
82AV, AJPROTOPORPHYRIN IX CONTAINING FEnon-polymer616.54Chemie (HEM)
Sequence viewer
Contents of the asymmetric unit
PolymersNumber of chains80
Total formula weight1614874.4
Non-Polymers*Number of molecules63
Total formula weight47978.1
All*Total formula weight1662852.5
*Water molecules are not included.

218853

PDB entries from 2024-04-24

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