4FDI
The molecular basis of mucopolysaccharidosis IV A
Entity
Entity ID | Chain ID | Description | Type | Chain length | Formula weight | Number of molecules | DB Name (Accession) | Biological source | Descriptive keywords |
1 | A, B | N-acetylgalactosamine-6-sulfatase | polymer | 502 | 56301.4 | 2 | UniProt (P34059) Pfam (PF00884) Pfam (PF14707) In PDB | Homo sapiens (human) | GALNS, Chondroitinsulfatase, Chondroitinase, Galactose-6-sulfate sulfatase, N-acetylgalactosamine-6-sulfate sulfatase, GalNAc6S sulfatase |
2 | A, B | 2-acetamido-2-deoxy-beta-D-glucopyranose | non-polymer | 221.2 | 4 | Chemie (NAG) | |||
3 | A, B | CALCIUM ION | non-polymer | 40.1 | 2 | Chemie (CA) | |||
4 | A, B | CITRIC ACID | non-polymer | 192.1 | 2 | Chemie (CIT) | |||
5 | A, B | GLYCEROL | non-polymer | 92.1 | 2 | Chemie (GOL) | |||
6 | water | water | 18.0 | 775 | Chemie (HOH) |
Sequence modifications
A, B: 27 - 522 (UniProt: P34059)
PDB | External Database | Details |
---|---|---|
His 523 | - | expression tag |
His 524 | - | expression tag |
His 525 | - | expression tag |
His 526 | - | expression tag |
His 527 | - | expression tag |
His 528 | - | expression tag |
Sequence viewer
Contents of the asymmetric unit
Polymers | Number of chains | 2 |
Total formula weight | 112602.9 | |
Non-Polymers* | Number of molecules | 10 |
Total formula weight | 1533.4 | |
All* | Total formula weight | 114136.3 |