2WWW

Crystal Structure of Methylmalonic Acidemia Type A Protein

Entity

Entity ID	Chain ID	Description	Type	Chain length	Formula weight	Number of molecules	DB Name (Accession)	Biological source	Descriptive keywords
1	A, B, C, D (A, B, C, D)	METHYLMALONIC ACIDURIA TYPE A PROTEIN, MITOCHONDRIAL	polymer	349	38718.9	4	UniProt (Q8IVH4) Pfam (PF03308)	HOMO SAPIENS (HUMAN)	METHYLMALONIC ACIDEMIA TYPE A
2	E, H, J (A, C, D)	NONAETHYLENE GLYCOL	non-polymer		414.5	3	Chemie (2PE)
3	F, G, I, K (A, B, C, D)	GUANOSINE-5'-DIPHOSPHATE	non-polymer		443.2	4	Chemie (GDP)
4	L, M, N, O (A, B, C, D)	water	water		18.0	87	Chemie (HOH)

Sequence modifications

A, B, C, D: 70 - 71 (PDB: 2WWW)
A, B, C, D: 72 - 418 (UniProt: Q8IVH4)

Contents of the asymmetric unit

Polymers	Number of chains	4
	Total formula weight	154875.5
Non-Polymers*	Number of molecules	7
	Total formula weight	3016.3
All*	Total formula weight	157891.7

*Water molecules are not included.