2WWW

Crystal Structure of Methylmalonic Acidemia Type A Protein

Entity

Entity ID	Chain ID	Description	Type	Chain length	Formula weight	Number of molecules	DB Name (Accession)	Biological source	Descriptive keywords
1	A, B, C, D (A, B, C, D)	METHYLMALONIC ACIDURIA TYPE A PROTEIN, MITOCHONDRIAL	polymer	349	38718.9	4	UniProt (Q8IVH4) Pfam (PF03308)	HOMO SAPIENS (HUMAN)	METHYLMALONIC ACIDEMIA TYPE A
2	E, H, J (A, C, D)	NONAETHYLENE GLYCOL	non-polymer		414.5	3	Chemie (2PE) PubChem (4867)
3	F, G, I, K (A, B, C, D)	GUANOSINE-5'-DIPHOSPHATE	non-polymer		443.2	4	Chemie (GDP) PubChem (136073927) PubChem (135398619) PubChem (135402030) PubChem (135431654) PubChem (135566337) PubChem (135760556) PubChem (136026707) PubChem (136053418) PubChem (136663964) PubChem (136664748) PubChem (136759848) PubChem (136759849) PubChem (136759850) PubChem (136836636) PubChem (136847074) PubChem (172898537)
4	L, M, N, O (A, B, C, D)	water	water		18.0	87	Chemie (HOH)

Sequence modifications

A, B, C, D: 70 - 71 (PDB: 2WWW)
A, B, C, D: 72 - 418 (UniProt: Q8IVH4)

Contents of the asymmetric unit

Polymers	Number of chains	4
	Total formula weight	154875.5
Non-Polymers*	Number of molecules	7
	Total formula weight	3016.3
All*	Total formula weight	157891.7

*Water molecules are not included.