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6K7Y

Intact human mitochondrial calcium uniporter complex with MICU1/MICU2 subunits

Functional Information from GO Data
ChainGOidnamespacecontents
A0051560biological_processmitochondrial calcium ion homeostasis
B0051560biological_processmitochondrial calcium ion homeostasis
C0051560biological_processmitochondrial calcium ion homeostasis
D0051560biological_processmitochondrial calcium ion homeostasis
E0036444biological_processcalcium import into the mitochondrion
E0051560biological_processmitochondrial calcium ion homeostasis
E1990246cellular_componentuniplex complex
F0036444biological_processcalcium import into the mitochondrion
F0051560biological_processmitochondrial calcium ion homeostasis
F1990246cellular_componentuniplex complex
G0036444biological_processcalcium import into the mitochondrion
G0051560biological_processmitochondrial calcium ion homeostasis
G1990246cellular_componentuniplex complex
H0036444biological_processcalcium import into the mitochondrion
H0051560biological_processmitochondrial calcium ion homeostasis
H1990246cellular_componentuniplex complex
I0005509molecular_functioncalcium ion binding
I0005515molecular_functionprotein binding
I0005739cellular_componentmitochondrion
I0005743cellular_componentmitochondrial inner membrane
I0005758cellular_componentmitochondrial intermembrane space
I0006816biological_processcalcium ion transport
I0006851biological_processmitochondrial calcium ion transmembrane transport
I0006952biological_processdefense response
I0019855molecular_functioncalcium channel inhibitor activity
I0031966cellular_componentmitochondrial membrane
I0034704cellular_componentcalcium channel complex
I0036444biological_processcalcium import into the mitochondrion
I0042802molecular_functionidentical protein binding
I0044284cellular_componentmitochondrial crista junction
I0046872molecular_functionmetal ion binding
I0046982molecular_functionprotein heterodimerization activity
I0051260biological_processprotein homooligomerization
I0051560biological_processmitochondrial calcium ion homeostasis
I0051561biological_processpositive regulation of mitochondrial calcium ion concentration
I0061891molecular_functioncalcium ion sensor activity
I0070509biological_processcalcium ion import
I0071277biological_processcellular response to calcium ion
I0072732biological_processcellular response to calcium ion starvation
I1900069biological_processregulation of cellular hyperosmotic salinity response
I1903852biological_processpositive regulation of cristae formation
I1990246cellular_componentuniplex complex
J0005509molecular_functioncalcium ion binding
J0006851biological_processmitochondrial calcium ion transmembrane transport
N0051560biological_processmitochondrial calcium ion homeostasis
O0051560biological_processmitochondrial calcium ion homeostasis
P0051560biological_processmitochondrial calcium ion homeostasis
Q0051560biological_processmitochondrial calcium ion homeostasis
R0036444biological_processcalcium import into the mitochondrion
R0051560biological_processmitochondrial calcium ion homeostasis
R1990246cellular_componentuniplex complex
S0036444biological_processcalcium import into the mitochondrion
S0051560biological_processmitochondrial calcium ion homeostasis
S1990246cellular_componentuniplex complex
T0036444biological_processcalcium import into the mitochondrion
T0051560biological_processmitochondrial calcium ion homeostasis
T1990246cellular_componentuniplex complex
U0036444biological_processcalcium import into the mitochondrion
U0051560biological_processmitochondrial calcium ion homeostasis
U1990246cellular_componentuniplex complex
V0005509molecular_functioncalcium ion binding
V0005515molecular_functionprotein binding
V0005739cellular_componentmitochondrion
V0005743cellular_componentmitochondrial inner membrane
V0005758cellular_componentmitochondrial intermembrane space
V0006816biological_processcalcium ion transport
V0006851biological_processmitochondrial calcium ion transmembrane transport
V0006952biological_processdefense response
V0019855molecular_functioncalcium channel inhibitor activity
V0031966cellular_componentmitochondrial membrane
V0034704cellular_componentcalcium channel complex
V0036444biological_processcalcium import into the mitochondrion
V0042802molecular_functionidentical protein binding
V0044284cellular_componentmitochondrial crista junction
V0046872molecular_functionmetal ion binding
V0046982molecular_functionprotein heterodimerization activity
V0051260biological_processprotein homooligomerization
V0051560biological_processmitochondrial calcium ion homeostasis
V0051561biological_processpositive regulation of mitochondrial calcium ion concentration
V0061891molecular_functioncalcium ion sensor activity
V0070509biological_processcalcium ion import
V0071277biological_processcellular response to calcium ion
V0072732biological_processcellular response to calcium ion starvation
V1900069biological_processregulation of cellular hyperosmotic salinity response
V1903852biological_processpositive regulation of cristae formation
V1990246cellular_componentuniplex complex
W0005509molecular_functioncalcium ion binding
W0006851biological_processmitochondrial calcium ion transmembrane transport
Functional Information from PROSITE/UniProt
site_idPS00018
Number of Residues13
DetailsEF_HAND_1 EF-hand calcium-binding domain. DLNGDGEVDmeEF
ChainResidueDetails
IASP231-PHE243
IASP421-PHE433

Functional Information from SwissProt/UniProt
site_idSWS_FT_FI1
Number of Residues2
DetailsMOD_RES: Phosphoserine => ECO:0007744|PubMed:18669648
ChainResidueDetails
JSER205
NVAL266-VAL283
OLEU234-TRP256
OVAL266-VAL283
PLEU234-TRP256
PVAL266-VAL283
QLEU234-TRP256
QVAL266-VAL283
WSER205
GSER53-SER64
HSER53-SER64
RSER53-SER64
SSER53-SER64
TSER53-SER64
USER53-SER64
NLEU234-TRP256

site_idSWS_FT_FI2
Number of Residues846
DetailsTOPO_DOM: Mitochondrial intermembrane => ECO:0000305|PubMed:26387864
ChainResidueDetails
ILYS53-GLN476
VLYS53-GLN476
GPHE65-ILE84
HPHE65-ILE84
RPHE65-ILE84
SPHE65-ILE84
TPHE65-ILE84
UPHE65-ILE84

site_idSWS_FT_FI3
Number of Residues20
DetailsBINDING: BINDING => ECO:0000255|PROSITE-ProRule:PRU00448, ECO:0000269|PubMed:24514027
ChainResidueDetails
IASP231
IGLU432
VASP231
VASN233
VASP235
VGLU237
VGLU242
VASP421
VASP423
VASN425
VGLU427
IASN233
VGLU432
IASP235
IGLU237
IGLU242
IASP421
IASP423
IASN425
IGLU427

site_idSWS_FT_FI4
Number of Residues8
DetailsMOD_RES: N6-acetyllysine => ECO:0000250|UniProtKB:Q3UMR5
ChainResidueDetails
ALYS332
BLYS332
CLYS332
DLYS332
NLYS332
OLYS332
PLYS332
QLYS332

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PDB entries from 2024-07-24

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