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1HH8

The active N-terminal region of p67phox: Structure at 1.8 Angstrom resolution and biochemical characterizations of the A128V mutant implicated in chronic granulomatous disease

Functional Information from GO Data
ChainGOidnamespacecontents
A0006909biological_processphagocytosis
A0016176molecular_functionsuperoxide-generating NADPH oxidase activator activity
A0043020cellular_componentNADPH oxidase complex
A0045730biological_processrespiratory burst
Functional Information from PDB Data
site_idAC1
Number of Residues13
DetailsBINDING SITE FOR RESIDUE FLC A1201
ChainResidue
AALA6
AGLU142
AHOH2158
AHOH2159
AHOH2160
AILE7
ATRP10
APRO35
AHIS36
AARG38
AILE39
ALYS138
AGLU141

Functional Information from SwissProt/UniProt
site_idSWS_FT_FI1
Number of Residues33
DetailsRepeat: {"description":"TPR 1"}
ChainResidueDetails

site_idSWS_FT_FI2
Number of Residues33
DetailsRepeat: {"description":"TPR 2"}
ChainResidueDetails

site_idSWS_FT_FI3
Number of Residues33
DetailsRepeat: {"description":"TPR 3"}
ChainResidueDetails

246704

PDB entries from 2025-12-24

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