3KE0
Crystal structure of N370S Glucocerebrosidase at acidic pH.
Summary for 3KE0
Entry DOI | 10.2210/pdb3ke0/pdb |
Related | 3KEH |
Descriptor | Glucosylceramidase, 2-acetamido-2-deoxy-beta-D-glucopyranose-(1-4)-2-acetamido-2-deoxy-alpha-D-glucopyranose, 2-acetamido-2-deoxy-beta-D-glucopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranose, ... (7 entities in total) |
Functional Keywords | tim barrel, alternative initiation, disease mutation, disulfide bond, gaucher disease, glycoprotein, glycosidase, hydrolase, ichthyosis, lipid metabolism, lysosome, membrane, sphingolipid metabolism |
Biological source | Homo sapiens (human) |
Total number of polymer chains | 2 |
Total formula weight | 113859.50 |
Authors | Wei, R.R.,Boucher, S.,Pan, C.Q.,Edmunds, T. (deposition date: 2009-10-23, release date: 2010-10-27, Last modification date: 2023-09-06) |
Primary citation | Wei, R.R.,Boucher, S.,Hughes, H.,Guziewica, N.,Pan, C.Q.,Edmunds, T. Crystal Structure of Glucocerebrosidase Containing the N370S Mutation, Implications for Chaperon Therapy To be Published, |
Experimental method | X-RAY DIFFRACTION (2.7 Å) |
Structure validation
Download full validation report