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2K1D

NMR Studies of a Pathogenic Mutant (D178N) of the Human Prion Protein

Summary for 2K1D
Entry DOI10.2210/pdb2k1d/pdb
Related1FO7 1QM1
NMR InformationBMRB: 15676
DescriptorMajor prion protein (1 entity in total)
Functional Keywordsprion protein, m/v 129 polymorphism, d178n, disease mutation, ffi, gss, glycoprotein, golgi apparatus, gpi-anchor, lipoprotein, membrane, unknown function
Biological sourceHomo sapiens (Human)
Total number of polymer chains1
Total formula weight16492.28
Authors
Mills, J.L.,Surewicz, K.,Surewicz, W.K.,Sonnichsen, F.D. (deposition date: 2008-02-29, release date: 2009-03-03, Last modification date: 2023-06-14)
Primary citationMills, J.L.,Surewicz, K.,Surewicz, W.K.,Sonnichsen, F.D.
Residue 129 polymorphism and conformational dynamics of familial prion diseases associated with the human prion protein variant D178N
To be Published,
Experimental method
SOLUTION NMR
Structure validation

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