Loading
PDBj
MenuPDBj@FacebookPDBj@X(formerly Twitter)PDBj@BlueSkyPDBj@YouTubewwPDB FoundationwwPDBDonate
RCSB PDBPDBeBMRBAdv. SearchSearch help

8JAW

Human MCC in MCCD state

Entity
Entity IDChain IDDescriptionTypeChain lengthFormula weightNumber of moleculesDB Name (Accession)Biological sourceDescriptive keywords
1A, C, E, F, H...
(A, C, E, F, H...)
Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrialpolymer72580584.06UniProt (Q96RQ3)
Pfam (PF00289)
Pfam (PF02786)
Pfam (PF02785)
Pfam (PF00364)
Homo sapiens (human)MCCase subunit alpha,3-methylcrotonyl-CoA carboxylase 1,3-methylcrotonyl-CoA carboxylase biotin-containing subunit,3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha
2B, D, G, I, J...
(B, D, G, I, J...)
Methylcrotonoyl-CoA carboxylase beta chain, mitochondrialpolymer56361406.06UniProt (Q9HCC0)
Pfam (PF01039)
Homo sapiens (human)MCCase subunit beta,3-methylcrotonyl-CoA carboxylase 2,3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit,3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta
3M, N, O, P, Q...
(A, C, E, F, H...)
5-(HEXAHYDRO-2-OXO-1H-THIENO[3,4-D]IMIDAZOL-6-YL)PENTANALnon-polymer228.36Chemie (BTI)
Sequence viewer
Contents of the asymmetric unit
PolymersNumber of chains12
Total formula weight851940.3
Non-Polymers*Number of molecules6
Total formula weight1369.9
All*Total formula weight853310.1
*Water molecules are not included.

247536

PDB entries from 2026-01-14

PDB statisticsPDBj update infoContact PDBjnumon