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1R47

Structure of human alpha-galactosidase

Entity
Entity IDChain IDDescriptionTypeChain lengthFormula weightNumber of moleculesDB Name (Accession)Biological sourceDescriptive keywords
1A, BAlpha-galactosidase Apolymer39845394.52UniProt (P06280)
Pfam (PF16499)
Pfam (PF17450)
In PDB
Homo sapiens (human)Melibiase, Alpha-D-galactoside galactohydrolase, Alpha-D-galactosidase A, Agalsidase alfa
2C2-acetamido-2-deoxy-beta-D-glucopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranosebranched424.41In PDB
GlyTouCan (G42666HT)
3D, Galpha-D-mannopyranose-(1-3)-[alpha-D-mannopyranose-(1-6)]alpha-D-mannopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranosebranched910.82In PDB
GlyTouCan (G21381MC)
4E, Halpha-D-mannopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranosebranched586.52In PDB
GlyTouCan (G62182OO)
5Falpha-D-mannopyranose-(1-3)-[alpha-D-mannopyranose-(1-6)]alpha-D-mannopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranose-(1-4)-[alpha-L-fucopyranose-(1-6)]2-acetamido-2-deoxy-beta-D-glucopyranosebranched1057.01In PDB
GlyTouCan (G64181RO)
6A, Bbeta-D-galactopyranosenon-polymer180.22Chemie (GAL)
7A, B1,2-ETHANEDIOLnon-polymer62.12Chemie (EDO)
8waterwater18.018Chemie (HOH)
Sequence viewer
Contents of the asymmetric unit
PolymersNumber of chains2
Total formula weight90789.1
BranchedNumber of molecules6
Total formula weight4476.1
Non-Polymers*Number of molecules4
Total formula weight484.4
All*Total formula weight95749.6
*Water molecules are not included.

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PDB entries from 2024-08-28

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