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9FAC

Additional cryo-EM structure of cardiac amyloid AL59 - mixed polymorph

Summary for 9FAC
Entry DOI10.2210/pdb9fac/pdb
Related9FAA
EMDB information50272
DescriptorMonoclonal immunoglobulin light chains (LC), 2-acetamido-2-deoxy-beta-D-glucopyranose (2 entities in total)
Functional Keywordssystemic al amyloid fibril, protein fibril
Biological sourceHomo sapiens
Total number of polymer chains5
Total formula weight70722.71
Authors
Schulte, T.,Speranzini, V.,Chaves-Sanjuan, A.,Milazzo, M.,Ricagno, S. (deposition date: 2024-05-10, release date: 2024-08-14)
Primary citationSchulte, T.,Chaves-Sanjuan, A.,Speranzini, V.,Sicking, K.,Milazzo, M.,Mazzini, G.,Rognoni, P.,Caminito, S.,Milani, P.,Marabelli, C.,Corbelli, A.,Diomede, L.,Fiordaliso, F.,Anastasia, L.,Pappone, C.,Merlini, G.,Bolognesi, M.,Nuvolone, M.,Fernandez-Busnadiego, R.,Palladini, G.,Ricagno, S.
Helical superstructures between amyloid and collagen in cardiac fibrils from a patient with AL amyloidosis.
To be published,
Experimental method
Structure validation

223790

數據於2024-08-14公開中

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