8PKG
ATTRV122I amyloid fibril from hereditary ATTR amloidosis
Summary for 8PKG
Entry DOI | 10.2210/pdb8pkg/pdb |
EMDB information | 17738 |
Descriptor | Transthyretin (1 entity in total) |
Functional Keywords | transthyretin, attr amyloidosis, attrv122i, amyloid fibril, misfolding disease, cryo-em, protein fibril |
Biological source | Homo sapiens (human) |
Total number of polymer chains | 6 |
Total formula weight | 82748.32 |
Authors | |
Primary citation | Steinebrei, M.,Baur, J.,Pradhan, A.,Kupfer, N.,Wiese, S.,Hegenbart, U.,Schonland, S.O.,Schmidt, M.,Fandrich, M. Common transthyretin-derived amyloid fibril structures in patients with hereditary ATTR amyloidosis. Nat Commun, 14:7623-7623, 2023 Cited by PubMed: 37993462DOI: 10.1038/s41467-023-43301-3 PDB entries with the same primary citation |
Experimental method | ELECTRON MICROSCOPY (2.99 Å) |
Structure validation
Download full validation report