7ASC
TGFBIp mutant A546T
Summary for 7ASC
Entry DOI | 10.2210/pdb7asc/pdb |
Related | 5nv6 |
Descriptor | Transforming growth factor-beta-induced protein ig-h3 (1 entity in total) |
Functional Keywords | granular corneal dystrophy, lattice corneal dystrophy, protein aggregation, extracellular matrix protein, protein fibril |
Biological source | Homo sapiens (Human) |
Total number of polymer chains | 2 |
Total formula weight | 130246.73 |
Authors | Andersen, G.R.,Nielsen, N.S.,Gadeberg, T.A.F. (deposition date: 2020-10-27, release date: 2020-12-23, Last modification date: 2024-01-31) |
Primary citation | Nielsen, N.S.,Gadeberg, T.A.F.,Poulsen, E.T.,Harwood, S.L.,Weberskov, C.E.,Pedersen, J.S.,Andersen, G.R.,Enghild, J.J. Mutation-induced dimerization of transforming growth factor-beta-induced protein may drive protein aggregation in granular corneal dystrophy. J.Biol.Chem., 297:100858-100858, 2021 Cited by PubMed: 34097874DOI: 10.1016/j.jbc.2021.100858 PDB entries with the same primary citation |
Experimental method | X-RAY DIFFRACTION (4.8 Å) |
Structure validation
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