6HUD
Cryo-EM structure of cardiac amyloid fibrils from an immunoglobulin light chain (AL) amyloidosis patient.
Summary for 6HUD
Entry DOI | 10.2210/pdb6hud/pdb |
EMDB information | 0274 |
Descriptor | Monoclonal immunoglobulin light chains (LC) (1 entity in total) |
Functional Keywords | immunoglobulin light chains; amyloid cardiomyopathy; ex-vivo cryo-em; helical reconstruction;, protein fibril |
Biological source | Homo sapiens |
Total number of polymer chains | 5 |
Total formula weight | 73104.32 |
Authors | Paissoni, C.,Camilloni, C. (deposition date: 2018-10-06, release date: 2019-03-27, Last modification date: 2019-04-03) |
Primary citation | Swuec, P.,Lavatelli, F.,Tasaki, M.,Paissoni, C.,Rognoni, P.,Maritan, M.,Brambilla, F.,Milani, P.,Mauri, P.,Camilloni, C.,Palladini, G.,Merlini, G.,Ricagno, S.,Bolognesi, M. Cryo-EM structure of cardiac amyloid fibrils from an immunoglobulin light chain AL amyloidosis patient. Nat Commun, 10:1269-1269, 2019 Cited by PubMed: 30894521DOI: 10.1038/s41467-019-09133-w PDB entries with the same primary citation |
Experimental method | ELECTRON MICROSCOPY (4 Å) |
Structure validation
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