4CHL
Human Ethylmalonic Encephalopathy Protein 1 (hETHE1)
Summary for 4CHL
Entry DOI | 10.2210/pdb4chl/pdb |
Descriptor | PERSULFIDE DIOXYGENASE ETHE1, MITOCHONDRIAL, FE (III) ION (3 entities in total) |
Functional Keywords | oxidoreductase, sulfide detoxification, glyoxalase ii family |
Biological source | HOMO SAPIENS (HUMAN) |
Cellular location | Cytoplasm : O95571 |
Total number of polymer chains | 2 |
Total formula weight | 52469.42 |
Authors | Pettinati, I.,Brem, J.,McDonough, M.A.,Schofield, C.J. (deposition date: 2013-12-03, release date: 2014-12-17, Last modification date: 2023-12-20) |
Primary citation | Pettinati, I.,Brem, J.,McDonough, M.A.,Schofield, C.J. Crystal structure of human persulfide dioxygenase: structural basis of ethylmalonic encephalopathy. Hum. Mol. Genet., 24:2458-2469, 2015 Cited by PubMed: 25596185DOI: 10.1093/hmg/ddv007 PDB entries with the same primary citation |
Experimental method | X-RAY DIFFRACTION (2.61 Å) |
Structure validation
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