3KE0
Crystal structure of N370S Glucocerebrosidase at acidic pH.
3KE0 の概要
エントリーDOI | 10.2210/pdb3ke0/pdb |
関連するPDBエントリー | 3KEH |
分子名称 | Glucosylceramidase, 2-acetamido-2-deoxy-beta-D-glucopyranose-(1-4)-2-acetamido-2-deoxy-alpha-D-glucopyranose, 2-acetamido-2-deoxy-beta-D-glucopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranose, ... (7 entities in total) |
機能のキーワード | tim barrel, alternative initiation, disease mutation, disulfide bond, gaucher disease, glycoprotein, glycosidase, hydrolase, ichthyosis, lipid metabolism, lysosome, membrane, sphingolipid metabolism |
由来する生物種 | Homo sapiens (human) |
タンパク質・核酸の鎖数 | 2 |
化学式量合計 | 113859.50 |
構造登録者 | |
主引用文献 | Wei, R.R.,Boucher, S.,Hughes, H.,Guziewica, N.,Pan, C.Q.,Edmunds, T. Crystal Structure of Glucocerebrosidase Containing the N370S Mutation, Implications for Chaperon Therapy To be Published, |
実験手法 | X-RAY DIFFRACTION (2.7 Å) |
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