2WKL
Velaglucerase alfa
2WKL の概要
エントリーDOI | 10.2210/pdb2wkl/pdb |
関連するPDBエントリー | 1OGS 1Y7V 2F61 2J25 2V3D 2V3E 2V3F |
分子名称 | GLUCOSYLCERAMIDASE, 2-acetamido-2-deoxy-beta-D-glucopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranose, 2-acetamido-2-deoxy-beta-D-glucopyranose, ... (5 entities in total) |
機能のキーワード | alternative initiation, sphingolipid metabolism, membrane, lysosome, hydrolase, ichthyosis, n-nonyl-deoxynojirimycin, n-nonyl-deoxynojirimycin alternative initiation, disulfide bond, pharmaceutical, gaucher disease, glycosidase, polymorphism, glycoprotein, alternative splicing, acid-beta-glucosidase, lipid metabolism, disease mutation, velaglucerase alfa |
由来する生物種 | HOMO SAPIENS (HUMAN) |
タンパク質・核酸の鎖数 | 2 |
化学式量合計 | 114117.58 |
構造登録者 | Brumshtein, B.,Salinas, P.,Peterson, B.,Chan, V.,Silman, I.,Sussman, J.L.,Savickas, P.J.,Robinson, G.S.,Futerman, A.H. (登録日: 2009-06-15, 公開日: 2009-09-22, 最終更新日: 2023-12-13) |
主引用文献 | Brumshtein, B.,Salinas, P.,Peterson, B.,Chan, V.,Silman, I.,Sussman, J.L.,Savickas, P.J.,Robinson, G.S.,Futerman, A.H. Characterization of Gene-Activated Human Acid-Beta-Glucosidase: Crystal Structure, Glycan Composition and Internalization Into Macrophages. Glycobiology, 20:24-, 2010 Cited by PubMed: 19741058DOI: 10.1093/GLYCOB/CWP138 主引用文献が同じPDBエントリー |
実験手法 | X-RAY DIFFRACTION (2.7 Å) |
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