2WCG
X-ray structure of acid-beta-glucosidase with N-octyl(cyclic guanidine)-nojirimycin in the active site
Summary for 2WCG
Entry DOI | 10.2210/pdb2wcg/pdb |
Descriptor | GLUCOSYLCERAMIDASE, beta-D-mannopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranose-(1-4)-2-acetamido-2-deoxy-beta-D-glucopyranose, alpha-L-fucopyranose, ... (7 entities in total) |
Functional Keywords | lipid metabolism, glucocerebrosidase, membrane, lysosome, hydrolase, glucosidase, glycoprotein, gaucher disease, sphingolipid metabolism |
Biological source | HOMO SAPIENS (HUMAN) |
Total number of polymer chains | 2 |
Total formula weight | 116536.46 |
Authors | Brumshtein, B.,Aguilar, M.,Garcia-Moreno, M.I.,Mellet, C.O.,Garcia-Fernandez, J.M.,Silman, I.,Shaaltiel, Y.,Aviezer, D.,Sussman, J.L.,Futerman, A.H. (deposition date: 2009-03-12, release date: 2009-11-24, Last modification date: 2023-12-13) |
Primary citation | Brumshtein, B.,Aguilar-Moncayo, M.,Garcia-Moreno, M.I.,Ortiz Mellet, C.,Garcia Fernandez, J.M.,Silman, I.,Shaaltiel, Y.,Aviezer, D.,Sussman, J.L.,Futerman, A.H. 6-Amino-6-Deoxy-5,6-Di-N-(N'-Octyliminomethylidene)Nojirimycin: Synthesis, Biological Evaluation, and Crystal Structure in Complex with Acid Beta-Glucosidase. Chembiochem, 10:1480-, 2009 Cited by PubMed: 19437524DOI: 10.1002/CBIC.200900142 PDB entries with the same primary citation |
Experimental method | X-RAY DIFFRACTION (2.3 Å) |
Structure validation
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