登録情報 データベース : PDB / ID : 6p7f 構造の表示 ダウンロードとリンクタイトル Human ABCC6 NBD2 R1459D mutant in Apo state 要素Multidrug resistance-associated protein 6 詳細 キーワード TRANSPORT PROTEIN / ABCC6 / NBD2 / Apo state / ATP-Binding Cassette transporter C6 / nucleotide binding domain 2機能・相同性 機能・相同性情報分子機能 ドメイン・相同性 構成要素
Defective ABCC6 causes PXE / inorganic diphosphate transport / inhibition of non-skeletal tissue mineralization / ATP transport / leukotriene transport / ABC-type glutathione-S-conjugate transporter / ABC-type glutathione S-conjugate transporter activity / intracellular phosphate ion homeostasis / response to sodium phosphate / ATPase-coupled inorganic anion transmembrane transporter activity ... Defective ABCC6 causes PXE / inorganic diphosphate transport / inhibition of non-skeletal tissue mineralization / ATP transport / leukotriene transport / ABC-type glutathione-S-conjugate transporter / ABC-type glutathione S-conjugate transporter activity / intracellular phosphate ion homeostasis / response to sodium phosphate / ATPase-coupled inorganic anion transmembrane transporter activity / phosphate ion homeostasis / トランスロカーゼ; 他の化合物の輸送を触媒; ヌクレオシド三リン酸の加水分解に伴う / response to magnesium ion / ATPase-coupled transmembrane transporter activity / calcium ion homeostasis / basal plasma membrane / ATP metabolic process / visual perception / ABC-family proteins mediated transport / transmembrane transport / gene expression / basolateral plasma membrane / response to xenobiotic stimulus / endoplasmic reticulum membrane / ATP hydrolysis activity / extracellular region / nucleoplasm / ATP binding / membrane / plasma membrane 類似検索 - 分子機能 Multi drug resistance-associated protein / : / ABC transporter transmembrane region / ABC transporter type 1, transmembrane domain / ABC transporter integral membrane type-1 fused domain profile. / ABC transporter type 1, transmembrane domain superfamily / ABC transporter-like, conserved site / ABC transporters family signature. / ABC transporter / ABC transporter-like, ATP-binding domain ... Multi drug resistance-associated protein / : / ABC transporter transmembrane region / ABC transporter type 1, transmembrane domain / ABC transporter integral membrane type-1 fused domain profile. / ABC transporter type 1, transmembrane domain superfamily / ABC transporter-like, conserved site / ABC transporters family signature. / ABC transporter / ABC transporter-like, ATP-binding domain / ATP-binding cassette, ABC transporter-type domain profile. / ATPases associated with a variety of cellular activities / AAA+ ATPase domain / P-loop containing nucleoside triphosphate hydrolase 類似検索 - ドメイン・相同性生物種 Homo sapiens (ヒト)手法 X線回折 / 分子置換 / 解像度 : 2.85003990159 Å 詳細データ登録者 Zheng, A. / Thibodeau, P.H. 資金援助 米国, 1件 詳細 詳細を隠す組織 認可番号 国 National Institutes of Health/National Institute of General Medical Sciences (NIH/NIGMS) GM122091 米国
引用ジャーナル : To Be Published タイトル : Structures of human ABCC6 NBD1 and NBD2著者 : Zheng, A. / Thibodeau, P.H. 履歴 登録 2019年6月5日 登録サイト : RCSB / 処理サイト : RCSB改定 1.0 2020年6月10日 Provider : repository / タイプ : Initial release改定 1.1 2023年10月11日 Group : Data collection / Database references / Refinement descriptionカテゴリ : chem_comp_atom / chem_comp_bond ... chem_comp_atom / chem_comp_bond / database_2 / pdbx_initial_refinement_model Item : _database_2.pdbx_DOI / _database_2.pdbx_database_accession
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