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-Structure paper
Title | X-Ray Structure of Human Acid-Beta-Glucosidase, the Defective Enzyme in Gaucher Disease |
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Journal, issue, pages | Embo Rep., Vol. 4, Page 704-, Year 2003 |
Publish date | May 13, 2003 (structure data deposition date) |
![]() | Dvir, H. / Harel, M. / Mccarthy, A.A. / Toker, L. / Silman, I. / Futerman, A.H. / Sussman, J.L. |
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Methods | X-ray diffraction |
Resolution | 2 Å |
Structure data | ![]() PDB-1ogs: |
Chemicals | ![]() ChemComp-SO4: ![]() ChemComp-NAG: ![]() ChemComp-HOH: |
Source |
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![]() | HYDROLASE / GAUCHER DISEASE / GLUCOSIDASE / GLUCOCEREBROSIDASE / CEREZYME HYDROLASE / GLYCOSIDASE / SPHINGOLIPID METABOLISM / GLYCOPROTE LYSOSOME / MEMBRANE / DISEASE MUTATI POLYMORPHISM / ALTERNATIVE INITIATION / PHARMACEUTICAL / ISRAEL STRUCTURAL PROTEOMICS CENTER / ISPC / STRUCTURAL GENOMICS |