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Title | Evaluating protein cross-linking as a therapeutic strategy to stabilize SOD1 variants in a mouse model of familial ALS. |
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Journal, issue, pages | Plos Biol., Vol. 22, Page e3002462-e3002462, Year 2024 |
Publish date | Jan 27, 2023 (structure data deposition date) |
Authors | Hossain, M.A. / Sarin, R. / Donnelly, D.P. / Miller, B.C. / Weiss, A. / McAlary, L. / Antonyuk, S.V. / Salisbury, J.P. / Amin, J. / Conway, J.B. ...Hossain, M.A. / Sarin, R. / Donnelly, D.P. / Miller, B.C. / Weiss, A. / McAlary, L. / Antonyuk, S.V. / Salisbury, J.P. / Amin, J. / Conway, J.B. / Watson, S.S. / Winters, J.N. / Xu, Y. / Alam, N. / Brahme, R.R. / Shahbazian, H. / Sivasankar, D. / Padmakumar, S. / Sattarova, A. / Ponmudiyan, A.C. / Gawde, T. / Verrill, D.E. / Yang, W. / Kannapadi, S. / Plant, L.D. / Auclair, J.R. / Makowski, L. / Petsko, G.A. / Ringe, D. / Agar, N.Y.R. / Greenblatt, D.J. / Ondrechen, M.J. / Chen, Y. / Yerbury, J.J. / Manetsch, R. / Hasnain, S.S. / Brown Jr., R.H. / Agar, J.N. |
External links | Plos Biol. / PubMed:38289969 |
Methods | X-ray diffraction |
Resolution | 1.665 - 1.77 Å |
Structure data | PDB-8ccx: PDB-8q6m: |
Chemicals | ChemComp-CU: ChemComp-ZN: ChemComp-SO4: ChemComp-UDI: ChemComp-DMS: ChemComp-HOH: ChemComp-ACT: |
Source |
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Keywords | OXIDOREDUCTASE / SOD1 / Amyotrophic Lateral Sclerosis / ALS / pharmacological chaperone / cross-linking / stabilization |