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-Structure paper
Title | Structural Comparison of Differently Glycosylated Forms of Acid-Beta-Glucosidase, the Defective Enzyme in Gaucher Disease |
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Journal, issue, pages | Acta Crystallogr. ,Sect. D, Vol. 62, Page 1458-, Year 2006 |
Publish date | Aug 16, 2006 (structure data deposition date) |
![]() | Brumshtein, B. / Wormald, M.R. / Silman, I. / Futerman, A.H. / Sussman, J.L. |
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Methods | X-ray diffraction |
Resolution | 2.9 Å |
Structure data | ![]() PDB-2j25: |
Chemicals | ![]() ChemComp-NAG: ![]() ChemComp-SO4: ![]() ChemComp-HOH: |
Source |
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![]() | HYDROLASE / PHARMACEUTICAL / GAUCHER DISEASE / DISEASE MUTATION / GLYCOSIDASE / SPHINGOLIPID / POLYMORPHISM / GLYCOPROTEIN / MEMBRANE / LYSOSOME / GLUCOSIDASE / GLUCOCEREBROSIDASE / ALTERNATIVE INITIATION / LIPID METABOLISM / CEREZYME HYDROLASE / SPHINGOLIPID METABOLISM |