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-Structure paper
Title | Crystal structure of human branched-chain alpha-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease. |
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Journal, issue, pages | Structure Fold. Des., Vol. 8, Page 277-291, Year 2000 |
Publish date | Jan 13, 2000 (structure data deposition date) |
![]() | AEvarsson, A. / Chuang, J.L. / Wynn, R.M. / Turley, S. / Chuang, D.T. / Hol, W.G. |
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Methods | X-ray diffraction |
Resolution | 2.7 Å |
Structure data | ![]() PDB-1dtw: |
Chemicals | ![]() ChemComp-MG: ![]() ChemComp-K: ![]() ChemComp-TPP: ![]() ChemComp-HOH: |
Source |
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![]() | OXIDOREDUCTASE / ThDP-binding fold / BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE |