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| Title | Crystal structure of human branched-chain alpha-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease. |
|---|---|
| Journal, issue, pages | Structure Fold. Des., Vol. 8, Page 277-291, Year 2000 |
| Publish date | Jan 13, 2000 (structure data deposition date) |
Authors | AEvarsson, A. / Chuang, J.L. / Wynn, R.M. / Turley, S. / Chuang, D.T. / Hol, W.G. |
External links | Structure Fold. Des. / PubMed:10745006 |
| Methods | X-ray diffraction |
| Resolution | 2.7 Å |
| Structure data | ![]() PDB-1dtw: |
| Chemicals | ![]() ChemComp-MG: ![]() ChemComp-K: ![]() ChemComp-TPP: ![]() ChemComp-HOH: |
| Source |
|
Keywords | OXIDOREDUCTASE / ThDP-binding fold / BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE |
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homo sapiens (human)
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