登録情報 | データベース: PDB / ID: 2r0m |
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タイトル | The effect of a Glu370Asp Mutation in Glutaryl-CoA Dehydrogenase on Proton Transfer to the Dienolate Intermediate |
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要素 | Glutaryl-CoA dehydrogenaseグルタリルCoAデヒドロゲナーゼ |
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キーワード | OXIDOREDUCTASE (酸化還元酵素) / Glutaryl-CoA Dehydrogenase (グルタリルCoAデヒドロゲナーゼ) / Flavoprotein (フラボタンパク質) / isomerase (異性化酵素) / Alternative splicing (選択的スプライシング) / Disease mutation / FAD / Mitochondrion (ミトコンドリア) / Polymorphism / Transit peptide |
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機能・相同性 | 機能・相同性情報
glutaryl-CoA dehydrogenase (ETF) / glutaryl-CoA dehydrogenase activity / tryptophan metabolic process / fatty-acyl-CoA biosynthetic process / fatty acid beta-oxidation using acyl-CoA dehydrogenase / Lysine catabolism / fatty-acyl-CoA binding / flavin adenine dinucleotide binding / ミトコンドリアマトリックス / ミトコンドリア類似検索 - 分子機能 Acyl-CoA dehydrogenases signature 1. / Acyl-CoA dehydrogenases signature 2. / Acyl-CoA dehydrogenase, conserved site / Butyryl-Coa Dehydrogenase, subunit A; domain 1 / Acyl-CoA dehydrogenase/oxidase, N-terminal domain / Acyl-CoA oxidase/dehydrogenase, middle domain superfamily / Butyryl-CoA Dehydrogenase, subunit A, domain 2 / Butyryl-CoA Dehydrogenase, subunit A; domain 2 / Acyl-CoA dehydrogenase/oxidase C-terminal / Acyl-CoA dehydrogenase/oxidase, N-terminal ...Acyl-CoA dehydrogenases signature 1. / Acyl-CoA dehydrogenases signature 2. / Acyl-CoA dehydrogenase, conserved site / Butyryl-Coa Dehydrogenase, subunit A; domain 1 / Acyl-CoA dehydrogenase/oxidase, N-terminal domain / Acyl-CoA oxidase/dehydrogenase, middle domain superfamily / Butyryl-CoA Dehydrogenase, subunit A, domain 2 / Butyryl-CoA Dehydrogenase, subunit A; domain 2 / Acyl-CoA dehydrogenase/oxidase C-terminal / Acyl-CoA dehydrogenase/oxidase, N-terminal / Acyl-CoA dehydrogenase, C-terminal domain / Acyl-CoA dehydrogenase, N-terminal domain / Acyl-CoA oxidase/dehydrogenase, middle domain / Acyl-CoA dehydrogenase, middle domain / Acyl-CoA dehydrogenase/oxidase, N-terminal domain superfamily / Butyryl-CoA Dehydrogenase, subunit A, domain 3 / Acyl-CoA dehydrogenase/oxidase, N-terminal and middle domain superfamily / Acyl-CoA dehydrogenase-like, C-terminal / Butyryl-CoA Dehydrogenase, subunit A; domain 3 / Up-down Bundle / Βバレル / Orthogonal Bundle / Mainly Beta / Mainly Alpha類似検索 - ドメイン・相同性 4-nitrobutanoic acid / フラビンアデニンジヌクレオチド / Glutaryl-CoA dehydrogenase, mitochondrial類似検索 - 構成要素 |
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生物種 | Homo sapiens (ヒト) |
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手法 | X線回折 / 分子置換 / 解像度: 2.7 Å |
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データ登録者 | Rao, K.S. / Fu, Z. / Albro, M. / Narayanan, B. / Baddam, S. / Lee, H.J. / Kim, J.J. / Frerman, F.E. |
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引用 | ジャーナル: Biochemistry / 年: 2007 タイトル: The effect of a Glu370Asp mutation in glutaryl-CoA dehydrogenase on proton transfer to the dienolate intermediate. 著者: Rao, K.S. / Fu, Z. / Albro, M. / Narayanan, B. / Baddam, S. / Lee, H.J. / Kim, J.J. / Frerman, F.E. |
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履歴 | 登録 | 2007年8月20日 | 登録サイト: RCSB / 処理サイト: RCSB |
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改定 1.0 | 2008年4月22日 | Provider: repository / タイプ: Initial release |
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改定 1.1 | 2011年7月13日 | Group: Version format compliance |
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改定 1.2 | 2021年10月20日 | Group: Database references / Derived calculations / カテゴリ: database_2 / struct_ref_seq_dif / struct_site Item: _database_2.pdbx_DOI / _database_2.pdbx_database_accession ..._database_2.pdbx_DOI / _database_2.pdbx_database_accession / _struct_ref_seq_dif.details / _struct_site.pdbx_auth_asym_id / _struct_site.pdbx_auth_comp_id / _struct_site.pdbx_auth_seq_id |
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改定 1.3 | 2023年8月30日 | Group: Data collection / Refinement description カテゴリ: chem_comp_atom / chem_comp_bond / pdbx_initial_refinement_model |
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